Resumo

BULL, J; BUNN, BK; GWENGU, P  e  LEBAKA, CS. Multidisciplinary Management is crucial in Pierre-Robin syndrome: A Case Report. S. Afr. dent. j. [online]. 2025, vol.80, n.9, pp.498-502. ISSN 0375-1562.  https://doi.org/10.17159/sadj.v80i09.21352.

BACKGROUND: Pierre-Robin syndrome (PRS) is a congenital disorder in which affected individuals present with micro/retrognathia, difficulty feeding, cleft lip/palate, glossoptosis and difficulty breathing. PRS affects between 1 in 8 500 to 1 in 20 000 births. The nature of the congenital defects results in patients presenting with numerous complications including malnutrition, aspiration pneumonia, recurrent local infections, dental abnormalities, respiratory problems as well as aesthetic and functional defects CASE REPORT: A 3-year-old female patient who was diagnosed with PRS at 6-months of age was referred to the Department of Operative Dentistry by the Department of Orthodontics with a main complaint of dental pain as well as the existing cleft palate DISCUSSION: The clinical needs for the alleviation of pain, surgical closure of clefts to facilitate nutritional intake, surgical intervention to prevent respiratory obstruction as well as the dental abnormalities which need to be managed and restored are all highlighted in this case presentation. Furthermore, the need for lifelong therapy, encouragement, monitoring and nurture within a supportive, stimulating environment are essential to improve the overall quality of life for patients with PRS CONCLUSION: The objective of documenting this case report is to demonstrate the diverse scope and nature of the health care team responsible for providing adequate treatment, rehabilitation and surgical intervention in the patient who has PRS. The need for holistic management through multidisciplinary collaboration is emphasised for patient and practitioner education

Palavras-chave : Pierre-Robin syndrome; congenital; micrognathia; glossoptosis; enamel hypoplasia; rampant decay; malocclusion; airway obstruction.

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