SA Journal of Radiology
versão On-line ISSN 2078-6778
versão impressa ISSN 1027-202X
ADROOS, Narosha; SMAL, Janet e SULEMAN, Farhana E.. Double trouble: Bilateral cerebral involvement in Sturge-Weber syndrome. S. Afr. J. radiol. (Online) [online]. 2015, vol.19, n.1, pp.1-4. ISSN 2078-6778. http://dx.doi.org/10.4102/SAJR.v19i1.760.
Sturge-Weber syndrome, also known as encephalotrigeminal angiomatosis or meningofacial angiomatosis, is characterised in its classical form by a congenital, usually unilateral, 'port-wine stain' (capillary naevus) on the face, convulsions, typical intracranial calcification and some degree of mental retardation and hemiparesis. The clinical correlation of intractable seizures with the presence of bilateral intracranial disease has management and prognostic implications, thus making the presence of bilateral disease an important factor to all those involved in the management of the child with Sturge-Weber syndrome.