SA Orthopaedic Journal
versão impressa ISSN 1681-150X
VERMAAK, DP. Arthrogryposis multiplex congenita of the upper limb. SA orthop. j. [online]. 2012, vol.11, n.1, pp. 34-39. ISSN 1681-150X.
The name arthrogryposis is derived from the Greek and means stiff joints (arthron = joint and grypos = stiff). Arthrogryposis represents a large group of disorders that present with joint contractures at birth. These congenital contracture syndromes total over 65 conditions with different clinical courses and pathological processes. Contracture syndrome groups can be divided into the following: • Group involving all four extremities - includes arthrogryposis multiplex congenita (AMC) and Larsen syndrome, usually with total body involvement. • Distal arthrogryposis - group predominantly or exclusively involving the hands and feet. Freeman-Sheldon whistling face is an example in this group. • Pterygia syndromes - identifiable skin webs cross the flexion aspects of knees, elbows and other joints. Multiple pterygias and popliteal pterygia belong to this group.
Palavras-chave : Arthrogryposis multiplex congenita; upper limb.