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South African Journal of Surgery
versão On-line ISSN 2078-5151
versão impressa ISSN 0038-2361
Resumo
JOUBERT, P e MIHALIK, M. Small bowel metastasis from embryonal rhabdomyosarcoma of the extremity - a case report. S. Afr. j. surg. [online]. 2023, vol.61, n.4, pp.48-50. ISSN 2078-5151. http://dx.doi.org/10.36303/sajs.4120.
Rhabdomyosarcoma is the most common soft tissue tumour in children and adolescents, but extremely rare in adults with comparatively worse outcomes. Metastatic disease is not uncommon, but intra-abdominal metastases are exceedingly rare. We report an unusual case of ileal metastases from an upper extremity rhabdomyosarcoma in a 17-year-old male who presented with abdominal pain during a routine follow-up visit. Laparotomy and ileocecectomy for a perforated ileal mass confirmed metastatic embryonal rhabdomyosarcoma with 1 out of 14 positive lymph node metastases. This case demonstrates that, although rare, intra-abdominal metastases should be considered when patients with a rhabdomyosarcoma present with abdominal complaints.
Palavras-chave : rhabdomyosarcoma; metastasis; adolescent; embryonal.